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Efficacy, Safety, and Tolerability of Zeleciment Basivarsen (DYNE-101) in Participants With Myotonic Dystrophy Type 1

About

Brief Summary

The purpose of the study is to assess the efficacy, safety, and tolerability of zeleciment basivarsen (DYNE-101) for the treatment of myotonic dystrophy 1 (DM1).

Primary Purpose
The main objective of the intervention(s) being evaluated by the clinical trial. Learn more
Treatment
Study Type
The nature of the investigation or investigational use for which clinical study information is being submitted. Learn more
Interventional
Phase
Phase 3

Eligibility

Gender
All
Healthy Volunteers
No
Minimum Age
16 Years
Maximum Age
N/A

Inclusion Criteria:

  • Diagnosis of DM1 confirmed by molecular genetics with trinucleotide repeat size greater than (>) 100. Historical results from clinical testing are acceptable.
  • Able to walk 10 meters and complete 5 times sit to stand independently (inserts or supports that don't go above the ankle are allowed).
  • Body mass index (BMI) less than (<) 35 kilograms per meter square (kg/m^2).

Exclusion Criteria:

  • A known diagnosis of congenital DM1.
  • History of major surgical procedure (based on Investigator judgment) within 12 weeks prior to the start of screening, with the exception of implanted pacemaker or defibrillator.
  • Use of glucagon-like peptide 1 (GLP-1) agonist/incretin medications including semaglutide, dulaglutide, liraglutide, exenatide, or tirzepatide within a period of 5 half-lives of the medication prior to performing screening assessments.

Note: Other inclusion and exclusion criteria may apply.

Study Stats
Protocol No.
26-0163
Category
Brain/Neurological Diseases
Genetic and Rare Diseases
Musculoskeletal Disorders
Principal Investigator
Perry B. Shieh, MD, PhD
Perry B. Shieh, MD, PhD
Neurology, Neuromuscular Medicine
Perry B. Shieh, MD, PhD
Contact
  • Dennis Fernando
Location
  • UCLA Westwood
For Providers
NCT No.
NCT07486934
For detailed technical eligibility, visit ClinicalTrials.gov.